Directori de persones
Fabien Delaspre

Fabien Delaspre

Grau: Doctor/a


fabien.delaspre(ELIMINAR)@udl.cat

ResearcherID: http://www.researcherid.com/rid/M-3654-2015

Publicacions

  • Sanz-Alcázar A; Britti E; Delaspre F; Medina-Carbonero M; Pazos-Gil M; Tamarit J; Ros J; Cabiscol E

    Mitochondrial impairment, decreased sirtuin activity and protein acetylation in dorsal root ganglia in Friedreich Ataxia models.

    Cellular And Molecular Life Sciences 81 12-12. .

    [doi:10.1007/s00018-023-05064-4]

  • Alves, R; Pazos-Gil, M; Medina-Carbonero, M; Sanz-Alcazar, A; Delaspre, F; Tamarit, J

    Evolution of an Iron-Detoxifying Protein: Eukaryotic and Rickettsia Frataxins Contain a Conserved Site Which Is Not Present in Their Bacterial Homologues.

    INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES 23 -. .

    [doi:10.3390/ijms232113151]

  • Medina-Carbonero, M; Sanz-Alcazar, A; Britti, E; Delaspre, F; Cabiscol, E; Ros, J; Tamarit, J

    Mice harboring the FXN I151F pathological point mutation present decreased frataxin levels, a Friedreich ataxia-like phenotype, and mitochondrial alterations.

    Cellular And Molecular Life Sciences 79 74-74. .

    [doi:10.1007/s00018-021-04100-5]

  • Tamarit J; Britti E; Delaspre F; Medina-Carbonero M; Sanz-Alcázar A; Cabiscol E; Ros J

    Mitochondrial iron and calcium homeostasis in Friedreich ataxia.

    IUBMB LIFE 73 543-553. .

    [doi:10.1002/iub.2457]

  • Britti E; Delaspre F; Sanz A; Medina-Carbonero M; Llovera M; Purroy R; Mincheva-Tasheva S; Tamarit J; Ros J

    Calcitriol increases frataxin levels and restores mitochondrial function in cell models of Friedreich Ataxia.

    BIOCHEMICAL JOURNAL 478 1-20. .

    [doi:10.1042/BCJ20200331]

  • Britti, E; Delaspre, F; Tamarit, J; Ros, J

    Calpain-Inhibitors Protect Frataxin-Deficient Dorsal Root Ganglia Neurons from Loss of Mitochondrial Na + /Ca 2+ Exchanger, NCLX, and Apoptosis.

    NEUROCHEMICAL RESEARCH 46 108-119. .

    [doi:10.1007/s11064-020-03020-3]

  • Rodríguez-Pascau L; Britti E; Calap-Quintana P; Dong YN; Vergara C; Delaspre F; Medina M; Tamarit J; Pallardó FV; Gonzalez-Cabo P; Ros J; Lynch DR; Martinell M; Pizcueta P

    PPAR gamma agonist leriglitazone improves frataxin-loss impairments in cellular and animal models of Friedreich Ataxia.

    NEUROBIOLOGY OF DISEASE 148 105162-105162. .

    [doi:10.1016/j.nbd.2020.105162]

  • Britti, Elena; Delaspre, Fabien; Tamarit, Jordi; Ros, Joaquim

    Mitochondrial calcium signalling and neurodegenerative diseases

    Neuronal Signaling 2 20180061-20180061. .

    [doi:10.1042/NS20180061]

  • Britti, E; Delaspre, F; Mincheva, S; Llovera, M; Tamarit, J; Ros, J

    Calcitriol as a supplement for Friedreich ataxia

    FEBS Open Bio 8 213-213. .

  • Britti, E; Delaspre, F; Feldman, A; Osborne, M; Greif, H; Tamarit, J; Ros, J

    Frataxin-deficient neurons and mice models of Friedreich ataxia are improved by TAT-MTScs-FXN treatment

    Journal Of Cellular And Molecular Medicine 22 834-848. .

    [doi:10.1111/jcmm.13365]

  • Purroy, R; Britti, E; Delaspre, F; Tamarit, J; Ros, J

    Mitochondrial pore opening and loss of Ca2+ exchanger NCLX levels occur after frataxin depletion

    BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE 1864 618-631. .

    [doi:10.1016/j.bbadis.2017.12.005]

  • Mangraviti A; Raghavan T; Volpin F; Skuli N; Gullotti D; Zhou J; Asnaghi L; Sankey E; Liu A; Wang Y; Lee DH; Gorelick N; Serra R; Peters M; Schriefer D; Delaspre F; Rodriguez FJ; Eberhart CG; Brem H; Olivi A; Tyler B

    HIF-1 alpha-Targeting Acriflavine Provides Long Term Survival and Radiological Tumor Response in Brain Cancer Therapy

    SCIENTIFIC REPORTS 7 14978-14978. .

    [doi:10.1038/s41598-017-14990-w]

Projectes

  • Étude comparative de souris I151F pour discerner les premières étapes de la pathogenèse del´Ataxie de Friedreich
  • Effet du Calcitriol dans un nouveau modèle murin pour l´AF de mutation ponctuelle I151F