Research > Neurosciences

Experimental Neuromuscular Pathology

Number of publications
45
Publications search
  • Tarabal O; Caraballo-Miralles V; Cardona-Rossinyol A; Correa FJ; Olmos G; Lladó J; Esquerda JE; Calderó J

    Mechanisms Involved in Spinal Cord Central Synapse Loss in a Mouse Model of Spinal Muscular Atrophy

    JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY 73 519-535. .

    [doi:10.1097/NEN.0000000000000074]

  • Sabado, Javier; Casanovas, Anna; Tarabal, Olga; Hereu, Marta; Piedrafita, Ldia; Caldero, Jordi; Esquerda, Josep E.

    Accumulation of Misfolded SOD1 in Dorsal Root Ganglion Degenerating Proprioceptive Sensory Neurons of Transgenic Mice with Amyotrophic Lateral Sclerosis

    BioMed Research International 2014 -. .

    [doi:10.1155/2014/852163]

  • Dachs E; Piedrafita L; Hereu M; Esquerda JE; Calderó J

    CHRONIC TREATMENT WITH LITHIUM DOES NOT IMPROVE NEUROMUSCULAR PHENOTYPE IN A MOUSE MODEL OF SEVERE SPINAL MUSCULAR ATROPHY

    NEUROSCIENCE 250 417-433. .

    [doi:10.1016/j.neuroscience.2013.07.026]

  • Sábado J; Casanovas A; HERNÁNDEZ ESTAÑOL, SARA; Piedrafita L; Hereu M; Esquerda JE

    Immunodetection of Disease-Associated Conformers of Mutant Cu/Zn Superoxide Dismutase 1 Selectively Expressed in Degenerating Neurons in Amyotrophic Lateral Sclerosis

    JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY 72 646-661. .

    [doi:10.1097/NEN.0b013e318297fd10]

  • Arque, Gloria; CASANOVAS, A.; Dierssen, Mara

    Dyrk1A Is Dynamically Expressed on Subsets of Motor Neurons and in the Neuromuscular Junction: Possible Role in Down Syndrome

    PLOS ONE 8 -. .

    [doi:10.1371/journal.pone.0054285]

  • Martinez-Hernandez, Rebeca; Bernal, Sara; Also-Rallo, Eva; Alias, Laura; Jesus Barcelo, Ma; Hereu, Marta; Esquerda, Josep E.; Tizzano, Eduardo F.

    Synaptic defects in type I spinal muscular atrophy in human development

    JOURNAL OF PATHOLOGY 229 49-61. .

    [doi:10.1002/path.4080]

  • Texido, Laura; Hernandez, Sara; Martin-Satue, Mireia; Povedano, Monica; Casanovas, Anna; Esquerda, Josep; Marsal, Jordi; Solsona, Caries

    Sera from amyotrophic lateral sclerosis patients induce the non-canonical activation of NMDA receptors "in vitro".

    NEUROCHEMISTRY INTERNATIONAL 59 954-964. .

    [doi:10.1016/j.neuint.2011.07.006]

  • Dachs, Elisabet; Hereu, Marta; Piedrafita, Lidia; Casanovas, Anna; Caldero, Jordi; Esquerda, Josep E.

    Defective neuromuscular junction organization and postnatal myogenesis in mice with severe spinal muscular atrophy.

    JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY 70 444-461. .

    [doi:10.1097/NEN.0b013e31821cbd8b]

  • Hernandez, Sara; Texido, Laura; Caldero, Jordi; Ciutat, Dolors; Piedrafita, Lidia; Casanovas, Anna; Blasi, Joan; Solsona, Carles; Povedano, Monica; Rojas, Ricardo; Illa, Isabel; Caress, James; Prevette, David; Oppenheim, Ronald W.; Milligan, Carol; Esquerda, Josep E.

    Increased intramuscular nerve branching and inhibition of programmed cell death of chick embryo motoneurons by immunoglobulins from patients with motoneuron disease.

    Journal Of Neuroimmunology 229 157-168. .

    [doi:10.1016/j.jneuroim.2010.07.028]

  • Caldero, J.; Brunet, N.; Tarabal, O.; Piedrafita, L.; Hereu, M.; Ayala, V.; Esquerda, J. E.

    Lithium prevents excitotoxic cell death of motoneurons in organotypic slice cultures of spinal cord.

    NEUROSCIENCE 165 1353-1369. .

    [doi:10.1016/j.neuroscience.2009.11.034]

  • Hernández S; Casanovas A; Piedrafita L; Tarabal O; Esquerda JE

    Neurotoxic species of misfolded SOD1G93A recognized by antibodies against the P2X4 subunit of the ATP receptor accumulate in damaged neurons of transgenic animal models of amyotrophic lateral sclerosis.

    JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY 69 176-187. .

    [doi:10.1097/NEN.0b013e3181cd3e33]

  • Brunet, Nuria; Tarabal, Olga; Esquerda, Josep E.; Caldero, Jordi

    Excitotoxic motoneuron degeneration induced by glutamate receptor agonists and mitochondrial toxins in organotypic cultures of chick embryo spinal cord.

    Journal Of Comparative Neurology 516 277-290. .

    [doi:10.1002/cne.22118]